Patients with pediatric neuromuscular disorders (muscular dystrophies, spinal muscular atrophy, metabolic myopathies) are surviving longer, and are requiring adult pulmonary providers to effectively transition care. The adult onset neuromuscular disorders are also increasing in prevalence (amyotrophic lateral sclerosis) and survival with advancing technologies in airway clearance and non-invasive ventilation (NIV). The session will address recognition of hypoventilatory respiratory insufficiency, implementation of stage specific respiratory assistive devices to maximize patient independence, quality of life and survival, and safely managing operative needs (routine and disease specific) after onset of respiratory insufficiency, bridging pediatric providers to adult pulmonary care and end of life issues.
CME credits and/or Certificates of Completion are not provided for this session.
1- Recognize hypoventilatory respiratory insufficiency associated with neuromuscular disease, with a goal of early diagnosis and implementation of assistive devices before overt respiratory failure, by disease stage
2- Learn to anticipate peri-operative changes, and adapt the assistive device usage to prevent respiratory complications while allowing appropriate surgical interventions
3- Understand the importance of transitions; from Pediatric to Adult Pulmonologists, and at end of life. Key concepts include communication, disease understanding, expectations and recognition of crisis points distinct from dying
Michelle Cao, DO: Avoiding the Cliff Fall: Recognizing and Understanding the Mechanics and Progression of Hypoventilation in Neuromuscular Respiratory Insufficiency
Karen A. Provost, DO, PhD: School, Camping, Sport and Travel: Maintaining Quality of Life by Implementation of Non-Invasive Ventilation by Disease Stage
David Zielinski, MD: Mucus Is Not Our Friend: Secretion Management in Neuromuscular Respiratory Failure
Howard B. Panitch, MD: The Big Leap of Faith: Smoothing the Transition From Pediatric to Adult Respiratory Care
Hemant Sawnani, MD: Safely Navigating the Perioperative Management of Neuromuscular Patients, Without Panicking Your Anesthesia Colleague
Joshua O. Benditt, MD: Ethical and End of Life Considerations in Chronic Respiratory Failure: Facing the Inevitable (For Now) With Quality and Autonomy
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